Forestier´s Syndrome, Diffuse idiopathic skeletal hiperostosis: Report of a case of oropharyngeal dysphagia with conservative treatment and literature review

Forestier´s Syndrome, Diffuse idiopathic skeletal hiperostosis: Report of a case of oropharyngeal dysphagia with conservative treatment and literature review

Main Article Content

Marta Elizabeth Osorio Fleitas
Blas Antonio Medina Ruíz
Blás Agustín Medina Izcurdia
Joaquín Julián Medina Izcurdia

Abstract

Forestier Syndrome is a rheumatological disease of unknown origin, which consist in calcification of different areas of the body, predominantly at the level of the anterior common vertebral ligament, where osteophytes capable of producing varied symptoms of variable intensity are formed. Normally asymptomatic, although, when it affects the cervical spine, the most common symptom is dysphagia.


A case of Forestier syndrome is presented who consulted for dysphagia in the Head and Neck Surgery Unit of the Otolaryngology Service of the Institute of Social Prevision, Asuncion, Paraguay. The semiology allowed to observe a submucosal bulge in the posterior wall of the oropharynx of 1,5 cm in diameter, which could be evaluated and confirmed by tomography.


Due to the low intensity of the symptoms and little impact on the general state, it was decided to carry out a conservative treatment with good results, after two years of clinical follow-up. In these cases, surgery occupies a secondary place, either before the failure of this conservative behavior or the progression of the symptoms.

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